증례
전음성 난청이 동반된 하악안면이골증 1례
신양호1,*, 이호진1, 김등래2, 고신우2
A Case of Conductive Hearing Difficulty on Treacher Collins Syndrome
Yang Ho Shin1,*, Ho Jin Lee1, Deung Rae Kim2, Sin Woo Ko2
1Department of Otorhinolaryngology, Kwang Myung Sung Ae Hospital, Gwangmyung, Korea
2Department of Otorhinolaryngology, Sung Ae Hospital, Seoul, Korea
*교신저자: 신양호, 423-711 경기도 광명시 철산3동 389 광명성애병원 이비인후과 전화: (02) 2680-7255·전송: (02) 2683-2431 E-mail:
drentshin@hanmail.net
© Copyright 2003 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Received: Aug 25, 2003; Accepted: Nov 05, 2003
Published Online: May 31, 2020
ABSTRACT
Treacher-Collins Syndrome, also called mandibulofacial dysostosis, affects the shape of the head and face. Small and slanting lower jaw, down slanting eyes, notched lower eyelids, lack or absence of the lower eyerash, hypoplasia or absence of the zygomatic processes and flattening of the frontonasal angle are characteristics of Treacher-Collins Syndrome. Most children with Treacher-Collins have normal development and intelligence. They have 40% hearing loss in each ear due to abnormalities of the outer and middle ear, which conduct sound to the nerve endings. This paper reviewed a case of bilateral conductive hearing loss on Treacher-Collins Syndrome. (J Clinical Otolaryngol 2003;14:302-305)
Keywords: 하악안면이골증; 전음성 난청
Keywords: Mandibulofacial dysostosis; Conductive; Hearing loss