Journal of Clinical Otolaryngology Head and Neck Surgery

The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery

J Clin Otolaryngol Head Neck Surg 2002; 13(2):220-224

pISSN: 1225-0244, eISSN: 2713-833X

DOI: https://doi.org/10.35420/jcohns.2002.13.2.220

증례

두개저, 부비동, 하비갑개, 비중격에 광범위하게 침범된 다골성 섬유성 이형성증 1례

최익수¹^,^*, 오지청¹, 전병훈¹, 안병주¹

A Case of Polyostotic Fibrous Dysplasia of the Skull Base, Paranasal Sinus, Inferior Turbinate and Septum

Ick Soo Choi¹^,^*, Ji Cheng Oh¹, Byung Hoon Jun¹, Byoung Ju Ahn¹

¹인제대학교 의과대학 이비인후과학교실

¹Department of Otolaryngology, Inje University College of Medicine, Seoul Paik Hospital, Seoul, Korea

^*교신저자: 최익수, 100-032 서울 중구 저동 2가 85번지 인제대학교 의과대학 서울백병원 이비인후과학교실 전화: (02) 2270-0070~2, 0075 전송: (02) 2270-0073 E-mail: cisoo99@yahoo.co.kr

© Copyright 2002 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Received: Aug 12, 2002; Accepted: Oct 02, 2002

Published Online: May 31, 2020

ABSTRACT

Fibrous dysplasia is considered as a benign disease of the bone having an unknown etiology, characterized by a slow progression. Medullary bone that is replaced by mildly to highly cellular tissue composed of irregular trabeculae of woven bone and spindle-shaped fibroblasts. Craniofacial involvement frequently affects the maxilla and frontal bone and induced local facial swelling, facial asymmetry and exophthalmos. Currently three general subtypes of disease are recognized：monostotic, polyostotic, and McCune-Albright syndrome. We present 15-year-old male with left proptosis, superior eyelid swelling and nasal obstruction. Our case demonstrated an extensive bony lesion involving bilateral frontal, ethmoid, sphenoid sinuses, left maxillary bone, inferior turbinate, septum, and skull base. Hence we report a case of polyostotic fibrous dysplasia with extensive bony involvement. (J Clinical Otolaryngol 2002;13:220-224)

Keywords: 섬유성 이형성증; 다발골성형 이형성증; 비강; 부비강; 두개저

Keywords: Fibrous dysplasia, Polyostotic; Panasal sinuses; Skull base; Nasal cavity