Journal of Clinical Otolaryngology Head and Neck Surgery
The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery
종설
청각신경병성 스펙트럼 장애
김진동1,*
Jin-Dong Kim1,*
Received: Sep 12, 2016; Revised: Oct 11, 2016; Accepted: Nov 21, 2016
Published Online: May 31, 2020
ABSTRACT
Auditory neuropathy spectrum disorder (ANSD) is a specific form of hearing loss characterized by normal or near-normal outer hair cell function but severely abnormal or completely absent afferent neural activity in the auditory pathway. This review is to provide physicians and clinicians with information about the disorder and to help them understand it. It includes descriptions of causes of ANSD, assessment tools used to diagnose ANSD, limitations in current tools to determine site(s) of lesion, and current evidence related to the management of individuals with ANSD. (J Clinical Otolaryngol 2016;27:246–261)
Keywords: 청각신경병성 스펙트럼 장애; 와우 전위; 이음향방사; 청성뇌간반응; 보청기; 인공와우
Keywords: Auditory neuropathy spectrum disorder; Cochlear microphonics; Otoacoustic emissions; Auditory brainstem response; Hearing aids; Cochlear implants