증례
측두골에 발생한 랑게르한스 세포 조직구증 2예
배우용1, 장윤석1, 홍숙희2, 강명구1,*
Two Cases of Langerhans Cell Histiocytosis of the Temporal Bone
Woo-Yong Bae1, Yoon-Seok Jang1, Suk-Hee Hong2, Myung-Koo Kang1,*
1Department of Otolaryngology-Head and Neck Surgery, Dong-A University, Busan, Korea
2Pathology, College of Medicine, Dong-A University, Busan, Korea
*교신저자: 강명구, 602-715 부산광역시 서구 동대신동 3가 1번지 동아대학교 의과대학 이비인후과학교실 전화: (051) 240-5428·전송: (051) 253-0712 E-mail:
mgkang@daunet.donga.ac.kr
© Copyright 2005 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Received: Apr 20, 2005; Accepted: May 30, 2005
Published Online: May 31, 2020
ABSTRACT
The most well-known childhood histiocytosis, previously known as histiocytosis X, is Langerhans cell histiocytosis and includes the clinical entities of eosinophilic granuloma, Hand-Schüller-Christian disease and Letterer-Siwe disease. The hallmark of this disease is the presence of a clonal proliferation of cells of the monocyte lineage containing the characteristic electron microscopic findings of a Langerhans cell. The skeleton is involved in 80% of patients and bone lesions may be single or numerous and are seen most commonly in the skull, especially in the temporal bone. Prognosis is relatively favorable. We have experienced two cases of Langerhans cell histiocytosis with temporal bone involvement which were treated surgically in two children. (J Clinical Otolaryngol 2005;16:132-135)
Keywords: 랑게르한스 세포 조직구증; 측두골; 수술요법
Keywords: Histiocytosis, Langerhans-cell; Temporal bone; Surgery
