Journal of Clinical Otolaryngology Head and Neck Surgery

The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery

J Clin Otolaryngol Head Neck Surg 2002; 13(1):122-126

pISSN: 1225-0244, eISSN: 2713-833X

DOI: https://doi.org/10.35420/jcohns.2002.13.1.122

증례

내이도협착 및 전정계이형성을 동반한 와우무형성 1예

김은석¹, 장백암¹^,^*, 강기석¹, 강정한¹

A Case of Cochlear Aplasia with Narrow Internal Auditory Canal and Dysplastic Vestibular System

Eun Seok Kim¹, Baik Ahm Chang¹^,^*, Ki Seok Kang¹, Jung Han Kang¹

¹서울위생병원 이비인후과

¹Department of Otolaryngology, Seoul Adventist Hospital, Seoul, Korea

^*교신저자: 장백암, 130-092 서울 동대문구 휘경 2동 29-1 서울위생병원 이비인후과 전화: (02) 2210-3559·전송: (02) 2210-3558 E-mail: stone007kr@yahoo.co.kr

© Copyright 2002 The Busan, Ulsan, Gyeoungnam Branch of Korean Society of Otolaryngology-Head and Neck Surgery. This is an Open-Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.

Received: Jan 02, 2002; Accepted: Mar 21, 2002

Published Online: May 31, 2020

ABSTRACT

Congenital anomalies of the inner ear are rare disease and the majority of them are difficult to diagnose during one’s life time because they are malformations limited to the membranous labyrinth. However, inner ear anomalies involving bony labyrinth can be detected in life time through radiogaphic imaging and it has been known to occupy 8-20% of patients with congenital sensorineural hearing loss. We experienced a rare case of inner ear anomaly, in which the cochlea was not formed, the lateral semicircular canal was not developed, the vestibule was dilated and the internal auditory canal was narrowed. (J Clinical Otolaryngol 2002;13:122-126)

Keywords: 감각신경성난청; 와우무형성; 전정이형성; 내이도협착

Keywords: Sensorineural hearing loss; Cochlear aplasia; Vestibular dysplasia; Narrow internal auditory canal